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Anti-GAA Antibody (monoclonal,2G7)

Acid alpha glucosidase | Acid maltase | Aglucosidase alfa | Alpha glucosidase | GAA | Glucosidase alpha acid | Glucosidase alpha | LYAG | P10253

分类:

一抗 - 单克隆抗体

说明书:

M01548

860元/50ul  1520元/100ul  2280元/150ul  

human,mouse,rat

WB,IHC-P,ICC/IF,FCM

Monoclonal

现货

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Product Brief

  • 产品概况

    货号 M01548
    产品名称 Anti-GAA Antibody (monoclonal,2G7)
    基因名 GAA
    抗体来源 Mouse
    克隆 Monoclonal
    抗体亚型 Mouse IgG2b
    免疫原 A synthetic peptide corresponding to a sequence at the N-terminus of human Synaptophysin(1-26aa MLLLADMDVVNQLVAGGQFRVVKEPL),identical to the related mouse and rat sequences.
    内容 Each vial contains 4mg Trehalose,0.9mg NaCl,0.2mg Na2HPO4,0.05mg NaN3.
    纯化方式 Immunogen affinity purified.
    产品形态 Lyophilized
    保存条件 12 months from date of receipt,-20℃ as supplied.6 months 2 to 8℃ after reconstitution.Avoid repeated freezing and thawing.
    背景资料 Lysosomal alpha-glucosidase is an enzyme that in humans is encoded by the GAA gene. This gene encodes lysosomal alpha-glucosidase,which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II,also known as Pompe's disease,which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.
    Uniprot ID GAA: P10253
    推荐配套的二抗和检测试剂 Boster recommends Enhanced Chemiluminescent Kit with anti-Rabbit IgG (EK1002) for Western blot, and HRP Conjugated anti-Rabbit IgG Super Vision Assay Kit (SV0001-1) for IHC(P). *Blocking peptide 可以联系我们购买。

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